Elosulfataasi alfan (Vimizim) hankinta

Deadline:N/A

Tender information
Finland
Type
Voluntary ex ante transparency
Procedure
Negotiated without a call for competition
Duration
06/07/2026 - 31/12/2028
Elosulfataasi alfa on rekombinantti ihmisen N-asetyyligalaktoosiamiini-6-sulfataasi (rhGALNS), joka on valmistettu yhdistelmä-DNA-tekniikalla kiinanhamsterin munasarjasoluviljelmässä. Elosulfataasi alfa korvaa puuttuvan N-asetyyligalaktosamiini-6-sulfataasin (GALNS) entsyymin ja vähentää glykosaminoglykaanien (kerataanisulfaatti ja kondroitiini-6-sulfaatti) kertymistä soluihin. Suomen markkinoilla on vain yksi myyntiluvallinen elosulfataasi alfavalmiste, Vimizim. Vimizim on tarkoitettu tyypin IVA mukopolysakkaridoosin (Morquion oireyhtymä A, Morquio A Syndrome, MPS IVA) hoitoon kaikenikäisillä potilailla. Hankinnan arvioitu arvo on noin 3 000 000 (ALV 0 %) euroa listahinnan mukaan arvioituna.
Buyer
HUS Group, the joint authority for Helsinki and Uusimaa
buyer-email@mail.com
organization number

Documents

Document name
Upload date
File size
First document.pdf
1 Jan 1970, 00:001 Bytes
Second document.pdf
1 Jan 1970, 00:001 Bytes
No time limit
Important dates
19 Jun - Publication date
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